Absent left main coronary artery in a case of pulmonary atresia-intact ventricular septum and right ventricle-dependent coronary circulation
Krokovay A, Knirsch W, Kelly-Geyer J, Cesnjevar R, Dave H (2022)
Publication Type: Journal article
Publication year: 2022
Journal
Book Volume: 15
Pages Range: 425-428
Journal Issue: 4
Abstract
Right ventricle-dependent coronary circulation coexisting with left main coronary atresia in the setting of pulmonary atresia-intact ventricular septum is rare. In the case described, the left coronary artery (LCA) origin from the aorta could not be found on conventional angiography or cardiac magnetic resonance imaging. During surgery, multiple LCA branches originating from the finger-like continuum of the primitive right ventricular sinusoidal network were observed. A Damus-Kaye-Stansel anastomosis and an aortopulmonary shunt operation were performed. Shunt takedown and a bidirectional Glenn anastomosis followed at 3 months of age. At 18 months follow-up, the child is thriving with stable hemodynamics and a saturation of 85%. Awareness about this rare coronary artery anomaly is necessary to prevent catastrophic consequences. The challenges, complications, and lessons learned while treating this rare variant are discussed.
Involved external institutions
Switzerland (CH)How to cite
APA:
Krokovay, A., Knirsch, W., Kelly-Geyer, J., Cesnjevar, R., & Dave, H. (2022). Absent left main coronary artery in a case of pulmonary atresia-intact ventricular septum and right ventricle-dependent coronary circulation. Annals of Pediatric Cardiology, 15(4), 425-428. https://doi.org/10.4103/apc.apc_232_21
MLA:
Krokovay, Anna, et al. "Absent left main coronary artery in a case of pulmonary atresia-intact ventricular septum and right ventricle-dependent coronary circulation." Annals of Pediatric Cardiology 15.4 (2022): 425-428.
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